Hereditary Angioedema (HAE)
Diagnosis and management of C1 inhibitor deficiency.
Reviewed by Dr Kola Tytler MBBS CertHE MBA MRCGP (General Practitioner)
Last reviewed: 21 October 2025
Clinical Guidelines
NICE CKS: Angio-oedema and anaphylaxis
National
NICE Technology Appraisal Guidance [TA738]: Berotralstat for preventing recurrent attacks of hereditary angioedemaNational
The international WAO/EAACI guideline for the management of hereditary angioedemaNational
BSACI guideline for the management of chronic urticaria and angioedemaLocal
C1 inhibitor deficiency: 2014 United Kingdom consensus documentLocal
The international WAO/EAACI guideline for the management of hereditary angioedema – The 2021 revision and updateLocal
The International/Canadian Hereditary Angioedema GuidelineLocal
US HAEA Medical Advisory Board 2020 Guidelines for the Management of Hereditary AngioedemaLocal
WAO Guideline for the Management of Hereditary AngioedemaLocal